Journal of Case Reports in Medical Science
 

Journal of Case Reports in Medical Science, ISSN No. : .., Vol.: 3, Issue.: 1

Case Study

CROW-FUKASE SYNDROME, A RARE CASE: FIRST OF ITS KIND REPORTED IN A TERTIARY HOSPITAL IN MAKURDI, NIGERIA

 

NWANNADI IKENNA ALEXANDER1*, ALAO OLUSAYO OLAYINKA1, OKOLI ROBERTSON1, ABA IYAJI HANNAH1 AND OKOLIE IFECHUKWUDI2

1Department of Haematology, College of Health Sciences, Benue State University, Makurdi, Nigeria.

2Department of Haematology, Benue State University Teaching Hospital, Makurdi, Benue State, Nigeria.

Abstracts

Crow-Fukase syndrome also known as POEMS syndrome or Takatsuki disease or PEP syndrome (Plasma cell dyscrasia, Endocrinopathy and Polyneuropathy) is a rare multisystem disorder that is associated with plasma cell neoplasm. The syndrome is made up of polyneuropathy, organomegaly, endocrinopathy, monoclonal gammamopathy, and skin changes. We report here the first case of Crow-Fukase syndrome in a five year old tertiary hospital, in the north central region of Nigeria.

Keywords :

Multisystem disorder; POEMS syndrome; plasma cell dyscrasia; monoclonal gammopathy.